腹腔镜双侧附件切除DSD患者双侧性腺肿瘤

                               
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A 17-year old female patient presented to the pediatric endocrinologist because of primary amenorrhea. After diagnostic evaluation an endocrinologist found female phenotype and male karyotype (46, XY). MR of the abdomen shows tumor of both gonads. Left gonad looked like testicle and right was ovary. The diagnosis of disorder of sexual development (DSD) was established.
Bilateral laparoscopic adnexectomy was performed.
Patohistological examination showed bilateral gonadoblastoma with components of dysgerminoma. There was no gonadal tissue in both removed specimens. TNM: T1bNXMX; Figo: 1b